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KMID : 0357920060400000200
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Korean Journal of Pathology
2006 Volume.40 No. 0 p.200 ~ p.200
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Retiform Hemangioendothelioma - A Case Report -
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Chu YC
Kim L/Choi SJ/Park IS/Han JY/Kim JM
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Abstract
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Retiform hemangioendothelioma (RH) is a locally aggressive, rarely metastasizing vascular lesion. RH is uncommon. Since its original description in 1994, only 20 cases have been reported. The age range is wide but it usually affects young adults with no sex predominance. The tumor involves predominantly the skin and subcutaneous tissue and shows predilection for the distal extremities, particularly the lower limb. RH of the maxilla is very rare. A 14-year-old man presented with frequent epistaxis for one year and fascial swelling of right cheek area for 1 month. Radiologically, computed tomography revealed wall enhancing mass in right infratemporal fossa with extension to right cavernous sinus and orbit apex. The tumor was incompletely resected and measured 5.0cm in diameter. The cut surface revealed whitish yellow solid appearance. Microscopic finding revealed characteristic elongated and narrow arborizing vascular channels arranged in a retiform pattern. The vessels were lined by monomorphic small hyperchromatic endothelial cells with hobnail appearance and focal papillae with hyaline collagenous cores. The intervening collagenous stroma appeared sclerotic, especially in the vicinity of the vascular channel and revealed focal prominent lymphocytic infiltration.
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